Enlarged Vestibular Aqueduct Syndrome: A Case Report
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Apr 12, 2018
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Abstract
Large vestibular aqueduct is the most frequent condition found in radiological imaging of patients with sensorineural hearing loss. The frequency of this syndrome continues to be underestimated, which has lead to underdiagnosis. The purpose of this case report and its discussion is to clarify the most important aspects of the clinical diagnosis, audiology and radiology, as well as rise attention to the importance of this entity as part of the differential diagnosis in hearing loss workup.
Keywords
vestibular aqueduct, hearing loss, sensorineural, conductiveacueducto vestibular, pérdida auditiva conductiva, pérdida auditiva sensorineural
References
1. Govaerts PJ, Casselman J, Daemers K, De Ceulaer G, Somers T,
Offeciers FE. Audiological findings in large vestibular aqueduct syndrome.
Int J Pediatr Otorhinolaryngol. 1999 Dec 15;51(3):157-64.
2. Marques SR, Ajzen S, D Ippolito G, Alonso L, Isotani S, Lederman H.
Morphometric analysis of the internal auditory canal by computed
tomography imaging. Iran J Radiol Q J Publ Iran Radiol Soc. 2012
Jun;9(2):71-8.
3. Valvassori GE, Clemis JD. The large vestibular aqueduct syndrome. The
Laryngoscope. 1978 May;88(5):723-8.
4. Wu C-C, Chen Y-S, Chen P-J, Hsu C-J. Common clinical features of
children with enlarged vestibular aqueduct and Mondini dysplasia. The
Laryngoscope. 2005 Jan;115(1):132-7.
5. Asma A, Anouk H, Luc VH, Brokx JPL, Cila U, Van De Heyning P.
Therapeutic approach in managing patients with large vestibular aqueduct
syndrome (LVAS). Int J Pediatr Otorhinolaryngol. 2010 May;74(5):474-81.
6. Berrettini S, Forli F, Bogazzi F, Neri E, Salvatori L, Casani AP, et al. Large
vestibular aqueduct syndrome: audiological, radiological, clinical, and
genetic features. Am J Otolaryngol. 2005 Dec;26(6):363-71.
7. Gopen Q, Zhou G, Whittemore K, Kenna M. Enlarged vestibular
aqueduct: review of controversial aspects. The Laryngoscope. 2011
Sep;121(9):1971-8.
8. Zhou G, Gopen Q, Kenna MA. Delineating the hearing loss in children
with enlarged vestibular aqueduct. The Laryngoscope. 2008
Nov;118(11):2062-6.
9. Vijayasekaran S, Halsted MJ, Boston M, Meinzen-Derr J, Bardo DME,
Greinwald J, et al. When is the vestibular aqueduct enlarged? A statistical
analysis of the normative distribution of vestibular aqueduct size. AJNR Am
J Neuroradiol. 2007 Jul;28(6):1133-8.
10. Santos S, Sgambatti L, Bueno A, Albi G, Suárez A, Domínguez MJ.
[Enlarged vestibular aqueduct syndrome: A review of 55 paediatric
patients]. Acta Otorrinolaringológica Esp. 2010 Oct;61(5):338-44.
11. Madden C, Halsted M, Benton C, Greinwald J, Choo D. Enlarged
vestibular aqueduct syndrome in the pediatric population. Otol Neurotol Off
Publ Am Otol Soc Am Neurotol Soc Eur Acad Otol Neurotol. 2003
Jul;24(4):625-32.
12. Mori T, Westerberg BD, Atashband S, Kozak FK. Natural history of
hearing loss in children with enlarged vestibular aqueduct syndrome. J
Otolaryngol-Head Neck Surg J Oto-Rhino-Laryngol Chir Cervico-Faciale.
2008 Feb;37(1):112-8.
13. Grimmer JF, Hedlund G, Park A. Steroid treatment of hearing loss in
enlarged vestibular aqueduct anomaly. Int J Pediatr Otorhinolaryngol. 2008
Nov;72(11):1711-5.
14. Harker LA, Vanderheiden S, Veazey D, Gentile N, McCleary E.
Multichannel cochlear implantation in children with large vestibular
aqueduct syndrome. Ann Otol Rhinol Laryngol Suppl. 1999 Apr;177:39-43.
Offeciers FE. Audiological findings in large vestibular aqueduct syndrome.
Int J Pediatr Otorhinolaryngol. 1999 Dec 15;51(3):157-64.
2. Marques SR, Ajzen S, D Ippolito G, Alonso L, Isotani S, Lederman H.
Morphometric analysis of the internal auditory canal by computed
tomography imaging. Iran J Radiol Q J Publ Iran Radiol Soc. 2012
Jun;9(2):71-8.
3. Valvassori GE, Clemis JD. The large vestibular aqueduct syndrome. The
Laryngoscope. 1978 May;88(5):723-8.
4. Wu C-C, Chen Y-S, Chen P-J, Hsu C-J. Common clinical features of
children with enlarged vestibular aqueduct and Mondini dysplasia. The
Laryngoscope. 2005 Jan;115(1):132-7.
5. Asma A, Anouk H, Luc VH, Brokx JPL, Cila U, Van De Heyning P.
Therapeutic approach in managing patients with large vestibular aqueduct
syndrome (LVAS). Int J Pediatr Otorhinolaryngol. 2010 May;74(5):474-81.
6. Berrettini S, Forli F, Bogazzi F, Neri E, Salvatori L, Casani AP, et al. Large
vestibular aqueduct syndrome: audiological, radiological, clinical, and
genetic features. Am J Otolaryngol. 2005 Dec;26(6):363-71.
7. Gopen Q, Zhou G, Whittemore K, Kenna M. Enlarged vestibular
aqueduct: review of controversial aspects. The Laryngoscope. 2011
Sep;121(9):1971-8.
8. Zhou G, Gopen Q, Kenna MA. Delineating the hearing loss in children
with enlarged vestibular aqueduct. The Laryngoscope. 2008
Nov;118(11):2062-6.
9. Vijayasekaran S, Halsted MJ, Boston M, Meinzen-Derr J, Bardo DME,
Greinwald J, et al. When is the vestibular aqueduct enlarged? A statistical
analysis of the normative distribution of vestibular aqueduct size. AJNR Am
J Neuroradiol. 2007 Jul;28(6):1133-8.
10. Santos S, Sgambatti L, Bueno A, Albi G, Suárez A, Domínguez MJ.
[Enlarged vestibular aqueduct syndrome: A review of 55 paediatric
patients]. Acta Otorrinolaringológica Esp. 2010 Oct;61(5):338-44.
11. Madden C, Halsted M, Benton C, Greinwald J, Choo D. Enlarged
vestibular aqueduct syndrome in the pediatric population. Otol Neurotol Off
Publ Am Otol Soc Am Neurotol Soc Eur Acad Otol Neurotol. 2003
Jul;24(4):625-32.
12. Mori T, Westerberg BD, Atashband S, Kozak FK. Natural history of
hearing loss in children with enlarged vestibular aqueduct syndrome. J
Otolaryngol-Head Neck Surg J Oto-Rhino-Laryngol Chir Cervico-Faciale.
2008 Feb;37(1):112-8.
13. Grimmer JF, Hedlund G, Park A. Steroid treatment of hearing loss in
enlarged vestibular aqueduct anomaly. Int J Pediatr Otorhinolaryngol. 2008
Nov;72(11):1711-5.
14. Harker LA, Vanderheiden S, Veazey D, Gentile N, McCleary E.
Multichannel cochlear implantation in children with large vestibular
aqueduct syndrome. Ann Otol Rhinol Laryngol Suppl. 1999 Apr;177:39-43.
How to Cite
Marin Gallego, G. L., Barragan Delgado, S., & Hernández González, S. (2018). Enlarged Vestibular Aqueduct Syndrome: A Case Report. Universitas Medica, 59(2). https://doi.org/10.11144/Javeriana.umed59-2.savd
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Case Reports