Cri Du Chat Syndrome: Considerations in Dentistry. A Systematic Review
https://orcid.org/0000-0002-7322-6129
Ana del Carmen Armas Vega
https://orcid.org/0000-0003-3800-8166
Álex Esteban Carrera Robalino
https://orcid.org/0000-0003-1049-7930
Adriana Patricia Paltas Miranda
https://orcid.org/0000-0003-3705-8778
Mayra Elizabeth Paltas Miranda
https://orcid.org/0000-0003-3441-6015
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Background: Cri du Chat syndrome (SCdC) is a low-prevalence genetic disorder. It is important that clinical dentists know about its craniofacial and stomatological characteristics, as well as considerations for an adequate treatment of these patients. Purpose: to identify recent advances in the diagnosis and treatment of patients with SCdC. Methods: in this systematic review, PubMed, SciELO, LiLACS, and TripDatabase were searched. Search terms were “Cri du Chat” and “cat howl syndrome and dentistry,” between 2003 and 2018. 25 articles that met the inclusion and exclusion criteria were obtained and analyzed. Results: the low frequency of appearance of the syndrome was confirmed. Representative craniofacial and oral characteristics associated with micrognathism and retrognathism that alter the patient's facial appearance were identified. Alterations such as dental crowding, malocclusion, and associated periodontal disease can be corrected and controlled with adequate oral hygiene and nutritional guidance for the patient and their parents. Conclusions: SCdC is rare. Its pathognomonic characteristics appear in childhood and adolescence, so they require more attention. Early detection makes it possible to propose an adequate treatment to improve the patients’ quality of life.
cat cry syndrome, child, Cri-du-Chat syndrome, dentistry, dentists, diagnostics, oral medicine, oral pathology, oral semiology, pediatric dentistry, syndromes, stomatognathic systemdiagnóstico, niño, odontología, odontología pediátrica, odontólogos, patología oral, medicina oral, síndromes, síndrome Cri du Chat, síndrome del maullido del gato, semiología oral, sistema estomatognáticocriança, dentistas, diagnósticos, medicina oral, odontologia, odontopediatria, patologia oral, semiologia oral, síndrome, síndrome do choro do gato, síndrome de Cri-du-Chat, sistema estomatognático
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