The Mayer-von Rokitansky-Küster-Hauser Syndrome
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Introduction: The Mayer-von Rokitansky-Küster-Hauser (MRKH) syndrome happens in approximately one of 5000 women born alive and is the commonest cause of congenital absence of the vagina.
Method:We present two cases handled surgically by means of abdomino-perineal correction with intestine interposition, performed by the specialties of Pediatric Gynecology and Coloproctology in the Hospital San Ignacio. Given the clinical and paraclinical findings, the creation of a neovagina it was considered the best therapeutic option for our patients, using a segment of sigmoid colon, since these patients did not have any degree of vaginal tube that could be dilatable.
Conclusions: The surgical approach in vaginal agenesis is one of the best types of treatments which we have to offer to these patients, among these the sigmoid neovagina is a technique with excellent results and relatively few complications, which has demonstrated to be adequately accepted by patients.
conductos de Müller, enfermedades de los genitales femeninos, cirugía colorrectal, Mullerian ducts, genital diseases, female, colorectal surgery,
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