Agenesia pulmonar
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nov 20, 2009
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Resumen
La agenesia pulmonar es una alteración poco frecuente, con predominio en el sexo femenino y sin preferencia por la lateralidad. Reportamos el caso de un recién nacido masculino con diagnóstico prenatal de hernia diafragmática. Al nacer, se descartó esta patología y se hizo una impresión diagnóstica de malformación adenomatoide quística (malformación congénita de la vía aérea pulmonar) vs. agenesia pulmonar. El paciente falleció a los seis días de vida y la necropsia confirmó una agenesia pulmonar.
Keywords
agenesia pulmonar, malformación adenomatoide quística, pulmonary agenesis, congenital cystic adenomatoid malformation.
References
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2. Askin F, Gilbert-Barness E. Respiratory system. In: Gilbert-Barness E. Potter´s pathology of the fetus, infant and child. Second edition. Mosby Elsevier; 2007;1073-56.
3. Shivanand G, Mukhophadyay S, Vashisht S. An unusual cause of recurrent respiratory tract infection: unilateral pulmonary agenesis. Eur J Radiol. 2003;48:67-9.
4. Nowaczyk MJM, Akamura LM, Waye J. DHCR7 and Smith-Lemli-Opitz syndrome. Clin Invest Med. 2001;24:311-7.
5. Pratap A, Agrawal A, Raja S, Khaniya S, Tiwari A, Kumar A. Fryns syndrome: a lethal mesoectodermal birth defect with variable expression in a pair of monozygotic twins. Singapore Med J. 2007;48:e106.
6. Banerjee S, Chatterjee S. Pulmonary agenesis with intrathoracic upper limb. J Pediatr Surgy. 1997;32:779-81.
7. Koseoglu N, Ucan ES, Cavdar C. Right lung agenesis and left lung bronchiectasis. Respir Med. 2005;1:110-2.
8. Nazaroglu H, Mete A, Bukte Y, Smsek M. Agenesis of the right lung presenting as a pulmonary infection. Clin Radiol. 2002;57:529-30.
9. Wright C. Congenital malformations of the lung. Current Diagnostic Pathology. 2006;12:191-201.
10. Fokstuen S, Schinzel A. Unilateral lobar pulmonary agenesis in sibs. J Med Genet. 2000;37;557-9.
11. Schwalbe E, Schneider P. Die morphologic der missbildungen des menschen und der thiere, Jena: G. Fisher 1912;3:812-22.
12. Berrocal T, Madrid C, Novo S, Gutiérrez J, Arjonilla A, Gómez-León
N. Congenital anomalies of the tracheobronchial tree, lung, and mediastinum: embryology, radiology, and pathology. Radiographics. 2003;24:e17.
13. Zylak CJ, Eyler WR, Spizarny DL, Stone CH. Developmental lung in the adult: radiologic-pathologic correlation. Radiographics. 2002;22:S25-43.
14. Paterson A. Imaging evaluation of congenital lung abnormalities in infants and children. Radiol Clin North Am. 2005;43:303-23.
15. Mata JM, Cáceres J. The dysmorphic lung: imaging findings. Eur Radiol. 1996;6:403-14.
2001;445-517.
2. Askin F, Gilbert-Barness E. Respiratory system. In: Gilbert-Barness E. Potter´s pathology of the fetus, infant and child. Second edition. Mosby Elsevier; 2007;1073-56.
3. Shivanand G, Mukhophadyay S, Vashisht S. An unusual cause of recurrent respiratory tract infection: unilateral pulmonary agenesis. Eur J Radiol. 2003;48:67-9.
4. Nowaczyk MJM, Akamura LM, Waye J. DHCR7 and Smith-Lemli-Opitz syndrome. Clin Invest Med. 2001;24:311-7.
5. Pratap A, Agrawal A, Raja S, Khaniya S, Tiwari A, Kumar A. Fryns syndrome: a lethal mesoectodermal birth defect with variable expression in a pair of monozygotic twins. Singapore Med J. 2007;48:e106.
6. Banerjee S, Chatterjee S. Pulmonary agenesis with intrathoracic upper limb. J Pediatr Surgy. 1997;32:779-81.
7. Koseoglu N, Ucan ES, Cavdar C. Right lung agenesis and left lung bronchiectasis. Respir Med. 2005;1:110-2.
8. Nazaroglu H, Mete A, Bukte Y, Smsek M. Agenesis of the right lung presenting as a pulmonary infection. Clin Radiol. 2002;57:529-30.
9. Wright C. Congenital malformations of the lung. Current Diagnostic Pathology. 2006;12:191-201.
10. Fokstuen S, Schinzel A. Unilateral lobar pulmonary agenesis in sibs. J Med Genet. 2000;37;557-9.
11. Schwalbe E, Schneider P. Die morphologic der missbildungen des menschen und der thiere, Jena: G. Fisher 1912;3:812-22.
12. Berrocal T, Madrid C, Novo S, Gutiérrez J, Arjonilla A, Gómez-León
N. Congenital anomalies of the tracheobronchial tree, lung, and mediastinum: embryology, radiology, and pathology. Radiographics. 2003;24:e17.
13. Zylak CJ, Eyler WR, Spizarny DL, Stone CH. Developmental lung in the adult: radiologic-pathologic correlation. Radiographics. 2002;22:S25-43.
14. Paterson A. Imaging evaluation of congenital lung abnormalities in infants and children. Radiol Clin North Am. 2005;43:303-23.
15. Mata JM, Cáceres J. The dysmorphic lung: imaging findings. Eur Radiol. 1996;6:403-14.
Cómo citar
Oyola, M., Gordillo, G., García, C. A., & Torres, D. (2009). Agenesia pulmonar. Universitas Medica, 51(1), 94–102. https://doi.org/10.11144/Javeriana.umed51-1.agpu
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Reportes de caso