Keywords
genital diseases
female
colorectal surgery
How to Cite
Abstract
Introduction: The Mayer-von Rokitansky-Küster-Hauser (MRKH) syndrome happens in approximately one of 5000 women born alive and is the commonest cause of congenital absence of the vagina.
Method:We present two cases handled surgically by means of abdomino-perineal correction with intestine interposition, performed by the specialties of Pediatric Gynecology and Coloproctology in the Hospital San Ignacio. Given the clinical and paraclinical findings, the creation of a neovagina it was considered the best therapeutic option for our patients, using a segment of sigmoid colon, since these patients did not have any degree of vaginal tube that could be dilatable.
Conclusions: The surgical approach in vaginal agenesis is one of the best types of treatments which we have to offer to these patients, among these the sigmoid neovagina is a technique with excellent results and relatively few complications, which has demonstrated to be adequately accepted by patients.
Morcel K, Camborieux L, Huerrier D. Mayer-Rokitansky-Küster-Hauser syndrome: review. Orphanet J Rare Dis. 2007;2:13.
Sultan C, Biason-Lauber A, Philibert P. Mayer-Rokitansky-Küster-Hauser syndrome: recent clinical and genetic findings. Gynecol Endocrinol. 2009;25(1):8-11.
Rajimwale A, Furness PD 3rd, Brant WO, Koyle MA. Vaginal construction using sigmoid colon in children and young adults. BJU Int. 2004 Jul;94(1):115-9.
Kapoor R, Kumar Sharma D, Jeet Sing K, Suri A, Singh P, Chaudhary H. Sigmoid vaginoplasty: long-term results. Urology. 2006;67(6):1212-5.
Barbosa G, Varela-Guzmán M. Adolescente con síndrome de Mayer-Rokitansky-Küster-Hauser: la importancia de un manejo integral multidisciplinario. Rev Colomb Obstet Ginecol. 2006;57(4): 305-11.
Frank RT. The formation of an artificial vagina without operation. Am J Obstet Gynecol 1938;35:1054–5.
Vecchietti G. Neovagina nella sindrome di Rokitansky-Ku¨ster-Hauser. Annu Ostet Gunecol. 1965;11:131-47.
Creatsas G, Deligeoroglou E, Christopoulos P. Creation of a neovagina after Creatsas modification of Williams vaginoplasty for the treatment of 200 patients with Mayer-Rokitansky-Kuster-Hauser syndrome. Fertil Steril. 2001 Nov;76(5):1036-40.
This journal is registered under a Creative Commons Attribution 4.0 International Public License. Thus, this work may be reproduced, distributed, and publicly shared in digital format, as long as the names of the authors and Pontificia Universidad Javeriana are acknowledged. Others are allowed to quote, adapt, transform, auto-archive, republish, and create based on this material, for any purpose (even commercial ones), provided the authorship is duly acknowledged, a link to the original work is provided, and it is specified if changes have been made. Pontificia Universidad Javeriana does not hold the rights of published works and the authors are solely responsible for the contents of their works; they keep the moral, intellectual, privacy, and publicity rights.
Approving the intervention of the work (review, copy-editing, translation, layout) and the following outreach, are granted through an use license and not through an assignment of rights. This means the journal and Pontificia Universidad Javeriana cannot be held responsible for any ethical malpractice by the authors. As a consequence of the protection granted by the use license, the journal is not required to publish recantations or modify information already published, unless the errata stems from the editorial management process. Publishing contents in this journal does not generate royalties for contributors.